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未经手术修复的 Bland-White-Garland 综合征麻醉管理1例并文献回顾
Authors Guo Q, Chen YJ, Huang H
Received 5 January 2019
Accepted for publication 27 June 2019
Published 16 July 2019 Volume 2019:12 Pages 2167—2176
DOI https://doi.org/10.2147/JPR.S200534
Checked for plagiarism Yes
Review by Single-blind
Peer reviewers approved by Dr Colin Mak
Peer reviewer comments 2
Editor who approved publication: Dr E Alfonso Romero-Sandoval
摘要:Bland-White-Garland 综合征(BWGS)是一种左冠状动脉异常起源于肺动脉的罕见且严重的先天性心脏病。在罕见的成年 BWGS 患者中,左冠状动脉由扩张的右冠状动脉侧支循环供血,当较高压力的冠状动脉血流流入较低压力的肺动脉导致“窃血”,严重影响心肌血流灌注。本研究报告一例 53 岁胆道结石男性患者,合并 BWGS、房颤、完全性左束支传导阻滞、慢性心力衰竭,在未经心脏手术修复冠状动脉畸形的情况下,在全身麻醉下行胆总管切开术并平稳度过围手术期。本文总结其诊治过程并回顾相关文献,归纳了 BWGS 的潜在病理生理机制和麻醉管理要点,以便对此罕见病诊治提供参考。
Keywords: anesthesia, Bland-White-Garland syndrome, left main coronary artery, right coronary artery, pulmonary artery, coronary steal